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VOLUME 13 , ISSUE 2 ( June, 2009 ) > List of Articles


Spontaneous rupture of adrenal pheochromocytoma in a patient with Von Recklinghausen′s disease

Negar Motayagheni, Ramin Azhough, Ali Reza Barband, Mitra Niafar, Hojjat Pourfathi

Keywords : Adrenal tumor, pheochromocytoma, von Recklinghausen′s disease, retroperitoneal hematoma

Citation Information : Motayagheni N, Azhough R, Barband AR, Niafar M, Pourfathi H. Spontaneous rupture of adrenal pheochromocytoma in a patient with Von Recklinghausen′s disease. Indian J Crit Care Med 2009; 13 (2):94-95.

DOI: 10.4103/0972-5229.56056

License: CC BY-ND 3.0

Published Online: 01-07-2012

Copyright Statement:  Copyright © 2009; The Author(s).


Spontaneous rupture of an adrenal pheochromocytoma is extremely rare and can be lethal because of dramatic changes in the circulation. We describe a 35-year-old Iranian female with previously diagnosed von Recklinghausen s disease who suffered spontaneous rupture of an adrenal pheochromocytoma, misdiagnosed as renal colic followed by an extensive retroperitoneal hematoma, irreversible hemodynamic shock, and death.

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