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VOLUME 20 , ISSUE 2 ( 2016 ) > List of Articles


Cerebral venous thrombosis presenting with intracerebral hemorrhage in a patient with paroxysmal nocturnal hemoglobinuria

Gentle Sunder Shrestha, Bishesh Sharma Poudyal, Gopal Sedain, Khandokar Imran Mahmud, Niranja Acharya

Keywords : Cerebral venous thrombosis, intracerebral hemorrhage, paroxysmal nocturnal hemoglobinuria

Citation Information : Shrestha GS, Poudyal BS, Sedain G, Mahmud KI, Acharya N. Cerebral venous thrombosis presenting with intracerebral hemorrhage in a patient with paroxysmal nocturnal hemoglobinuria. Indian J Crit Care Med 2016; 20 (2):117-119.

DOI: 10.4103/0972-5229.175948

License: CC BY-ND 3.0

Published Online: 01-08-2013

Copyright Statement:  Copyright © 2016; The Author(s).


Cerebral venous thrombosis (CVT) is an uncommon cause of stroke. Paroxysmal nocturnal hemoglobinuria (PNH) is a rare type of hemolytic anemia, frequently associated with thrombophilia. PNH may rarely present with CVT. Approximately, one-third of the patients with CVT develop cerebral hemorrhage. Here, we present a rare combination of CVT presenting with intracerebral hemorrhage in a patient with PNH. High index of suspicion is needed to avoid misdiagnosis. Patient was successfully managed with anticoagulation therapy.

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