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VOLUME 26 , ISSUE 6 ( June, 2022 ) > List of Articles


Porphyria-induced Postpartum Reversible Posterior Encephalopathy Syndrome

Shri R Sharma, Baiakmenlang Synmon, Yasmeen Hynniewtaya

Keywords : Acute intermittent porphyria, Encephalopathy, Postpartum period, Seizures

Citation Information : Sharma SR, Synmon B, Hynniewtaya Y. Porphyria-induced Postpartum Reversible Posterior Encephalopathy Syndrome. Indian J Crit Care Med 2022; 26 (6):728-730.

DOI: 10.5005/jp-journals-10071-24253

License: CC BY-NC 4.0

Published Online: 20-06-2022

Copyright Statement:  Copyright © 2022; The Author(s).


Acute intermittent porphyria (AIP) is a rare condition that needs to be kept in mind where its early recognition, conservative management, and removal of the precipitating factor are the key factors in its management. This “little imitator” presented with varied symptoms is often misdiagnosed. The diagnosis requires a strong index of suspicion as choosing an antiepileptic medication in the management of seizure requires a judicial choice to avoid precipitation of the underlying illness.

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