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VOLUME 16 , ISSUE 1 ( January, 2012 ) > List of Articles

CASE REPORT

An unusual case of pleural-based tumor with life-threatening post-operative complication

Satinder K. Jain, Sai Kiran Chaudhuri

Keywords : Factor IX deficiency, hemophilia B, pleural hematoma, pseudotumor

Citation Information : Jain SK, Chaudhuri SK. An unusual case of pleural-based tumor with life-threatening post-operative complication. Indian J Crit Care Med 2012; 16 (1):48-51.

DOI: 10.4103/0972-5229.94436

License: CC BY-ND 3.0

Published Online: 00-01-2012

Copyright Statement:  Copyright © 2012; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

A 57-year-old male presented with hemoptysis of 4 years duration and a gradually increasing pleural mass on chest X-ray. The mass was causing pressure effects on the liver and the lungs. To rule out malignancy, thoracotomy was performed, which revealed large, thick-walled hematoma. Complete excision of mass was performed. Post-operative course was complicated by massive pleural bleeding requiring massive blood transfusions and re-exploratory thoracotomy. Subsequent tests revealed factor IX deficiency and, hence, he was managed with recombinant factor IX concentrate. This case stresses upon the fact that hereditary bleeding disorders may be diagnosed even in late adulthood with atypical presentations such as pseudotumor in pleural space. Moreover, hemophilia B may present with normal APTT levels making the diagnosis even more difficult.


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